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Juvenile idiopathic arthritis-its rare presentation
1Department of Pediatrics, Institute of Post Graduate Medical Education and Research, Kolkata, India. jbghosh@yahoo.com
Indian Journal of Pediatrics
|June 1, 2011
Summary
Systemic onset juvenile idiopathic arthritis (SOJIA) can present with unusual symptoms like severe neck pain and respiratory issues. This case highlights cervical spondylitis and myocarditis as rare SOJIA manifestations, impacting cardiac function.
Area of Science:
- Pediatrics
- Rheumatology
- Cardiology
Background:
- Systemic onset juvenile idiopathic arthritis (SOJIA) is a rare autoimmune disease.
- Cardiovascular involvement in SOJIA typically includes pericarditis.
- Cervical spine involvement is uncommon in SOJIA.
Observation:
- A pediatric patient presented with fever, severe neck pain, and stiffness.
- Respiratory distress developed shortly after illness onset.
- The patient exhibited cervical spondylitis without peripheral joint disease.
Findings:
- Myocarditis was diagnosed, leading to congestive cardiac failure.
- Pericarditis was also present, a more common cardiovascular manifestation of SOJIA.
- The case demonstrated unusual patterns of SOJIA presentation.
Implications:
- Highlights the diverse clinical spectrum of SOJIA.
- Emphasizes the need for early recognition of atypical cardiovascular and musculoskeletal manifestations.
- Informs diagnostic approaches for pediatric patients with unexplained fever, neck pain, and cardiac symptoms.
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