Rare concurrence of apical hypertrophic cardiomyopathy and effusive constrictive pericarditis

Satoshi Okayama1, Tsunenari Soeda, Ayako Seno

  • 1First department of internal medicine, Nara medical university, Nara, Japan.

Insights

This study diagnosed apical hypertrophic cardiomyopathy (HCM) with concurrent effusive constrictive pericarditis in a patient with prior tuberculosis. Further research is needed to understand this rare cardiac condition.

Area of Science:

  • Cardiology
  • Cardiovascular Imaging
  • Pathophysiology

Background:

  • A 78-year-old male with a history of pulmonary tuberculosis presented for cardiac function evaluation.
  • Preoperative assessment revealed complex cardiac abnormalities requiring detailed investigation.

Purpose of the Study:

  • To diagnose the underlying cardiac condition in a patient with complex findings.
  • To investigate the interplay between hypertrophic cardiomyopathy and pericardial disease.

Main Methods:

  • Echocardiography was performed for initial cardiac assessment.
  • Cardiac cine magnetic resonance imaging (MRI) was utilized for detailed structural and functional evaluation.
  • Cardiac late gadolinium-enhanced MRI was employed to assess pericardial inflammation and fibrosis.

Main Results:

  • Findings included apical hypertrophic cardiomyopathy (HCM), thickened visceral pericardium, and a large pericardial effusion.
  • Late gadolinium-enhanced MRI indicated pericardial inflammation or fibrosis.
  • The patient was diagnosed with apical HCM and concurrent effusive constrictive pericarditis.

Conclusions:

  • Apical HCM coexisting with effusive constrictive pericarditis is a rare diagnosis.
  • The pathophysiology of this combined condition requires further investigation.
  • This case highlights the importance of advanced cardiac imaging in diagnosing complex cardiovascular diseases.

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