Related Experiment Video
Updated: May 31, 2026

Murine Bilateral Renal Lymphadenectomy
Published on: December 30, 2025
Bilateral renal artery stenosis and epidermal nevus syndrome in a child
Fahad Alsohim1, Pauline Abou-Jaoude, Jean Ninet
1Service de néphrologie, rhumatologie et dermatologie pédiatriques, Hôpital Femme Mère Enfant, centre de référence des maladies rénales rares, Hospices Civils de Lyon, 59 boulevard Pinel, 69500 Bron, France. alsohim-md@hotmail.com
Abstract:
Epidermal nevus syndrome is a rare congenital sporadic neuro-ectodermic disorder, characterized by the presence of epidermal nevi in association with various developmental abnormalities of the skin, eyes, nervous, skeletal, cardiovascular and urogenital systems. We describe a 5-year-old boy with conjunctival lipodermoid, cervical and facial sebaceous nevi who presented at 3 years of age with hypertension due to bilateral renal artery stenosis together with multiple vascular anomalies (aorta, celiac trunk, superior mesenteric artery) as shown by magnetic resonance angiography. Systemic arterial hypertension was difficult to control despite combined anti-hypertensive drugs and the surgical repair of the aortic coarctation.
Related Concept Videos
Nephrotic Syndrome I : Introduction
Imaging Studies VII: Vascular Imaging
Nephrons
External Anatomy of the Kidney
The kidneys are located in the retroperitoneal space on either side of the vertebral column, protected posteriorly by the 11th and 12th ribs. The right kidney sits slightly lower than the left owing to the presence of the liver...
Renal Corpuscle
Glomerulus: Structure and Function
The glomerulus is a tiny, intricate network of capillaries located at the beginning of the nephron. It's enveloped by the Bowman's capsule and receives its blood supply from an afferent arteriole, which divides into numerous capillaries...
The Retinoblastoma Gene
The first-ever tumor suppressor gene called Rb was identified in retinoblastoma - a rare eye tumor in children. In inherited forms of the disease, a child inherits one defective copy of the Rb gene, which predisposes them to retinoblastoma. However,...

