Erythroderma desquamativa of Leiner (clinical case)

Newborn at the age of 1 month and 10 days was examined in our Department in accordance with the request of Children's Hospital pediatrician for a diagnosis and prescription of adequate treatment. Anamnesis revealed that the child was born from parents (the second child) who are close relatives to each other (cousins, the Muslims - inbreeding). According to parents, the first child was born healthy, grow and develop without pathological abnormalities. At the birth of their second child, the changes in baby's skin appeared a month after birth. According to the father, during pregnancy, the baby's mother was injured (falling) followed by removal of hemorrhagic fluid from the pelvic cavity. On admission to our Department, the whole skin of newborn was brightly hyperemic, infiltrated and heavily shelled. On the scalp there were concentrations of yellow-gray color "fat" scales, resembling the bark or shell, going down on the forehead and brow. A child's face had masklike appearance. In some locations, in the parietal and frontal regions, after the removal of flakes the baldness was observed. The folds of the lower body (perineum, buttocks) were swollen, brightly hyperemic, macerated and soaked. In the middle of the folds were deep, difficult to heal fractures.