[Melkersson-Rosenthal syndrome in Curschmann-Steinert dystrophia myotonica]

We report the case of a 52-year-old female patient who suffered both from myotonic dystrophy (Curschmann-Steinert disease) and Melkersson-Rosenthal syndrome. Both syndromes showed the full-blown clinical features as well as the typical histology. In addition to the possibility that the appearance of the two syndromes together was a mere coincidence, we also consider the possibility that there was a hereditary diencephalic disorder present that linked together some of the minor manifestations of both syndromes.