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Updated: May 13, 2026
Anterior High-Resolution Optical Coherence Tomography in the Diagnosis and Therapeutic Monitoring of Ocular Surface Squamous Neoplasia
Published on: August 9, 2024
Primary dermatofibrosarcoma protuberans of orbit--a rare entity
Tashnin Rahman1, Kasturi Bhattacharjee, Jagannath Dev Sarma
1Dr. B. Borooah Cancer Institute, Regional Cancer Centre, Department of Head and Neck Oncology, Assam, Guwahati, India. drtashnin@yahoo.in
Abstract:
Primary Dermatofibrosarcoma Protuberance (DFSP) is a rare neoplasm of dermal origin. Though it is a locally aggressive tumor with high recurrence rate, however distant metastasis can also occur. Orbital DFSP is an uncommon phenomenon. It has been reported due to distant metastasis or invasion from adjacent structures but Primary Orbital DFSP is a unique entity in itself. Herein we report a rare case of primary DFSP of the orbit in a 70-year- old lady who underwent orbital exenteration. Histopathology examination (HPE) revealed spindle cells arranged in storiform pattern and immunohistochemistry (IHC) revealed CD34 positive and S100 negative.
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