Pre-operative magnetic resonance imaging in Lhermitte-Duclos disease

A 30-year-old woman presented with a 2.5 year history of symptoms and signs of raised intracranial pressure and unsteadiness of gait. CT showed a non-enhancing hypodense mass lesion in the left cerebellar hemisphere with compression and displacement of the fourth ventricle to the right and hydrocephalus of the third and lateral ventricles. Magnetic resonance imaging showed increased signal intensity in the mass lesion with the preservation of the gyral pattern on T2 weighted sequence. Imaging after gadolinium-DTPA injection showed non-enhancement and slight hypointensity of the lesion on T1 weighted sequence. These MRI findings are helpful in the preoperative diagnosis of Lhermitte-Duclos disease and allow the planning of an appropriate line of treatment for this rare condition.