[Febrile ulceronecrotic Mucha-Habermann disease]

Area of Science:

• Dermatology
• Pathology

Background:

• Pityriasis lichenoides et varioliformis acuta (PLEVA), pityriasis lichenoides chronica (PLC), and febrile ulceronecrotic Mucha-Habermann disease (FUMHD) are spectrums of the same disease.
• FUMHD is a rare, potentially lethal condition characterized by rapidly progressing papules that ulcerate and form necrotic plaques, accompanied by hemorrhagic vesicles, pustules, high fever, and systemic symptoms.

Observation:

• A 16-year-old male presented with fever and erythematous papules with crusts.
• The patient's clinical presentation and subsequent pathological examination confirmed the diagnosis of FUMHD.

Findings:

• Pathological study confirmed the diagnosis of FUMHD in the reported case.
• Initial treatment with prednisone was unsuccessful.

Implications:

• Minocycline demonstrated efficacy in treating FUMHD, suggesting it as a viable therapeutic option.
• This case underscores the importance of prompt diagnosis and appropriate treatment for FUMHD to prevent severe outcomes.