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Granulomatosis with polyangiitis can cause periaortitis and pericarditis
Mari Miyawaki1, Seitaro Oda1, Kenichiro Hirata1
1Department of Diagnostic Radiology Faculty of Life Sciences Kumamoto University 1-1-1 Honjyo Chuo-ku, Kumamoto 860-8556 Japan.
Clinical Case Reports
|October 14, 2017
Summary
Granulomatosis with polyangiitis (GPA) involves respiratory tract inflammation and small vessel vasculitis. However, GPA can also affect larger arteries, causing conditions like periaortitis and pericarditis.
Area of Science:
- Rheumatology
- Internal Medicine
- Pathology
Background:
- Granulomatosis with polyangiitis (GPA) is a vasculitis primarily affecting small vessels.
- GPA typically involves the respiratory tract with necrotizing granulomatous inflammation.
Purpose of the Study:
- To highlight that GPA, despite its classification, can manifest in larger arteries.
- To emphasize the diverse arterial involvement in GPA.
Main Methods:
- Review of clinical presentations and pathological findings in GPA patients.
- Analysis of literature concerning GPA's vascular manifestations.
Main Results:
- GPA characteristically involves necrotizing granulomatous inflammation of the respiratory tract and necrotizing vasculitis of small vessels.
- Cases of GPA presenting with periaortitis and pericarditis, indicative of larger artery involvement, were observed.
Conclusions:
- Physicians must consider that GPA can affect arteries of all sizes, not exclusively small vessels.
- Recognizing the spectrum of GPA vascular involvement is crucial for accurate diagnosis and management.