[Hour-glass craniofacial teratoma (author's transl)]

A male infant was born with a voluminous left jugal swelling identified by biopsy on the 8th day as a mature benign teratoma. Further investigations were conducted because of mild exophthalmia, including an electro-encephalogram and craniofacial computer tomography. An enormous frontotemporal intracranial extension of the tumor was discovered on the same side. The tumor was completely excised at the age of 1 month by a two-stage operation : neurosurgical followed by maxillofacial eight days later. The postoperative course was uneventful. There was no relapse after one year but because of the consequences of intracranial excision the prognosis was very poor. The authors discuss this case and review those in the published literature in order to describe the diagnosis, treatment, and prognosis of this extremely rare craniofacial teratoma of the newborn.