Cochlear implantation after radiation therapy for acoustic neuroma

Neurofibromatosis type 2 (NF-2) represents the complex issue of hearing restoration after treatment for a patient with bilateral acoustic neuromas. This scenario is difficult for skull base teams considering that all treatment options (including observation of tumors) pose a risk to the patient for further or total hearing loss. In this case of a patient with bilateral deafness, restoration options were auditory brainstem or cochlear implantation (CI). The deciding factor for CI was based on the presence of a functioning cochlear nerve and blood supply. Ultimately, treatment with radiation therapy and subsequent CI proved effective as evidenced by dramatic improvement in communication (with lip reading cues) and speech perception on 1-year audiologic testing. Radiosurgery followed by CI may represent a potential emerging option for patients with NF-2.