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A rare cause of heart failure
Dominika Zoltowska1, Jagadeesh Kumar Kalavakunta2
1Department of Internal Medicine Western Michigan University Homer Stryker School of Medicine 300 Portage Street Kalamazoo 49007 Michigan.
Clinical Case Reports
|June 9, 2018
Summary
Noncompaction cardiomyopathy (NCCM) is a rare heart failure cause. Left ventricle NCCM prevalence varies, but biventricular NCCM is extremely rare, with few reported cases.
Area of Science:
- Cardiology
- Genetics
- Heart Failure Research
Background:
- Noncompaction cardiomyopathy (NCCM) is a rare genetic heart muscle disease.
- It is an increasingly recognized cause of heart failure.
- NCCM can affect one or both ventricles.
Purpose of the Study:
- To summarize the current understanding of noncompaction cardiomyopathy.
- To highlight the prevalence of left ventricle and biventricular involvement.
Main Methods:
- Review of existing echocardiographic studies on NCCM prevalence.
- Analysis of reported cases of biventricular noncompaction cardiomyopathy.
Main Results:
- Prevalence of left ventricle NCCM ranges from 0.014% to 1.3% based on echocardiography.
- Biventricular involvement in NCCM is exceptionally rare, with very few cases documented.
Conclusions:
- Noncompaction cardiomyopathy is a significant cause of heart failure.
- While left ventricular NCCM has a variable prevalence, biventricular NCCM is exceedingly uncommon.
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