Glaucoma in children with facial port wine stain

Nader Hussein Lotfy Bayoumi1, Eman Nabil Elsayed1

  • 1Ophthalmology Department, Faculty of Medicine, Alexandria University, Alexandria, Egypt.

Insights

Children with facial port wine stains face a significant risk of developing glaucoma. Early surgical intervention for this condition shows a high success rate with few complications.

Area of Science:

  • Ophthalmology
  • Pediatric Ophthalmology
  • Medical Genetics

Background:

  • Facial port wine stains are congenital vascular malformations.
  • Ocular involvement, including glaucoma, can be associated with facial port wine stains.
  • Early detection and management are crucial for preserving vision in affected children.

Purpose of the Study:

  • To describe the clinical presentation of glaucoma in children with facial port wine stains.
  • To evaluate the surgical treatment and outcomes for glaucoma in this pediatric population.

Main Methods:

  • Retrospective chart review of 22 children (44 eyes) with facial port wine stains.
  • Data collected included demographics, ophthalmic examination findings, and treatments.
  • Outcome measures focused on glaucoma diagnosis and surgical success rates.

Main Results:

  • 34% of eyes were diagnosed with glaucoma, 30% as glaucoma suspects, and 36% with no glaucoma.
  • The average intraocular pressure in glaucomatous eyes was 20.6 mmHg.
  • Surgical intervention for glaucoma had a 91% success rate with a low complication rate.

Conclusions:

  • Glaucoma is a significant risk in children with facial port wine stains, potentially not apparent at initial presentation.
  • Affected eyes often present with clear corneas.
  • Surgical treatment for glaucoma in this cohort is effective and generally safe.
Abstract

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