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Primary coronary artery pseudoaneurysm in a patient with familial hypercholesterolemia

Toshiki Fujiyoshi1, Masaki Kano1, Hitoshi Ogino1

  • 1Department of Cardiovascular Surgery Tokyo Medical University Tokyo Japan.

Clinical Case Reports
|October 19, 2019
PubMed

Insights

Rare coronary artery pseudoaneurysms were successfully repaired in a young patient with heterozygous familial hypercholesterolemia (FH). Direct closure of intimal defects using aneurysmorrhaphy provided a successful treatment outcome.

Area of Science:

  • Cardiovascular Surgery
  • Vascular Medicine
  • Genetics

Background:

  • Coronary artery pseudoaneurysms are rare vascular abnormalities.
  • Familial hypercholesterolemia (FH) is a genetic disorder that increases cardiovascular risk.
  • Young patients with FH may present with complex cardiovascular conditions.

Observation:

  • A young patient diagnosed with heterozygous familial hypercholesterolemia presented with a rare primary coronary artery pseudoaneurysm.
  • The pseudoaneurysm required a minimally invasive surgical intervention.

Findings:

  • Successful surgical repair of the coronary artery pseudoaneurysm was achieved.
  • The procedure involved direct closure of intimal defects.
  • Aneurysmorrhaphy was the specific surgical technique employed.

Implications:

  • This case demonstrates the feasibility of aneurysmorrhaphy for treating coronary artery pseudoaneurysms in young patients.
  • Effective management of such rare conditions in genetically predisposed individuals is crucial.
  • Direct intimal defect closure offers a viable therapeutic option, potentially reducing complications.

Keywords:
coronary artery aneurysmheterozygous familial hypercholesterolemiapseudoaneurysm

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