Unusual Ventriculo-Arterial Alignments and Connections.

Area of Science:

• Pediatric Cardiology
• Congenital Heart Surgery
• Cardiac Anatomy

Background:

• Anatomically corrected malposition (ACM) is a rare congenital heart defect.
• Complex cases often involve associated anomalies like ventricular septal defects (VSD) and subaortic stenosis.
• Management strategies for ACM with complex lesions require careful consideration.

Purpose of the Study:

• To present a unique case of ACM with VSD and subaortic stenosis.
• To describe a staged biventricular repair approach for this complex condition.
• To enhance understanding of unusual ventriculo-arterial alignments.

Main Methods:

• Case report presentation.
• Surgical management via staged biventricular repair.
• Detailed anatomical and hemodynamic assessment.

Main Results:

• Successful staged biventricular repair was achieved.
• The patient's condition was managed effectively through the described strategy.
• Clarification of ventriculo-arterial relationships in this rare anomaly.

Conclusions:

• Staged biventricular repair is a viable option for ACM with VSD and subaortic stenosis.
• This case highlights the importance of tailored surgical approaches for complex congenital heart defects.
• Further understanding of unusual ventriculo-arterial alignments can improve surgical outcomes.