Tenosynovial Giant Cell Tumor in an Infant

Shawhin Shahriari1, Ashley Ederle2, James Botros3

  • 1Department of Surgery, Division of Plastic, Reconstructive, Hand, and Burn Surgery.

Insights

A rare infant tumor, tenosynovial giant cell tumor (TGCT), diffuse type, was found in the temporalis muscle. This extracranial mass was successfully treated with surgical excision in a 16-month-old child.

Area of Science:

  • Pediatric Oncology
  • Surgical Pathology
  • Head and Neck Surgery

Background:

  • Tenosynovial giant cell tumor (TGCT), diffuse type, is a rare neoplastic proliferation of joints and tendons.
  • Extracranial presentations of TGCT are uncommon, particularly in infants.
  • Malignant-appearing extracranial masses in infants require prompt diagnosis and management.

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