Cystic fibrosis year in review 2019: Section 3 multisystem-based care and research

Adrienne P Savant1,2, Susanna A McColley3,4,5

  • 1Division of Pulmonary Medicine, Children's Hospital of New Orleans, New Orleans, Louisiana, USA.

Pediatric Pulmonology
|November 19, 2020
PubMed

Insights

This review summarizes 2019 research on cystic fibrosis (CF) care, focusing on multisystem manifestations. It highlights advancements in CF management and treatment for patients and families.

Area of Science:

  • Medical Research
  • Pulmonology
  • Genetics

Background:

  • 2019 saw significant research publications relevant to cystic fibrosis (CF) care.
  • This article is the third in a series reviewing CF advancements.
  • Previous reviews covered CFTR modulators and pulmonary/airway disease.

Purpose of the Study:

  • To provide an overview of key research from 2019 concerning cystic fibrosis.
  • To focus on the multisystem aspects of CF care.
  • To inform healthcare professionals and families about recent developments.

Main Methods:

  • Literature review of research published in 2019.
  • Synthesis of findings related to multisystem manifestations of CF.
  • Categorization of studies based on previous review topics (modulators, pulmonary, infections).

Main Results:

  • Numerous studies offer valuable insights for CF professionals and families.
  • Focus on the broad impact of CF beyond the lungs.
  • Integration of findings from prior reviews on modulators and pulmonary disease.

Conclusions:

  • The year 2019 yielded important research for comprehensive CF care.
  • Understanding multisystem involvement is crucial for improving patient outcomes.
  • Continued research is vital for advancing the care of individuals with CF and their families.

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