Giant Right Ventricular Fibroma: Prenatal Diagnosis and Partial Resection in Early Infancy

Area of Science:

• Cardiology
• Pediatric Cardiology
• Cardiac Surgery

Background:

• Congenital cardiac fibromas are exceedingly rare cardiac tumors.
• Prenatal diagnosis of these tumors is infrequently reported.
• Cardiac fibromas can present as symptomatic or asymptomatic masses.

Purpose of the Study:

• To report a rare case of a symptomatic giant right ventricular fibroma diagnosed prenatally.
• To describe the diagnostic modalities and successful surgical management of a congenital cardiac fibroma in early infancy.
• To highlight the importance of prenatal diagnosis and timely intervention for congenital cardiac tumors.

Main Methods:

• Prenatal ultrasound at 33 weeks gestation identified a cardiac mass.
• Postnatal diagnosis was confirmed using echocardiogram and cardiac magnetic resonance imaging (CMR).
• The infant underwent partial surgical resection of the right ventricular fibroma.

Main Results:

• A giant cardiac fibroma was identified in the right ventricle during prenatal screening.
• The diagnosis was confirmed postnatally, revealing a symptomatic mass.
• Partial surgical resection resulted in an uneventful recovery for the infant.
• Hemodynamic stability was achieved after surgical intervention.

Conclusions:

• Congenital cardiac fibromas, though rare, require careful prenatal diagnosis and management.
• Early surgical intervention can lead to favorable outcomes in infants with symptomatic cardiac fibromas.
• This case underscores the feasibility of managing prenatally diagnosed cardiac fibromas in early infancy.