Bladder and urethral duplication and a bladder exstrophy plate with omphalocele in a female child

Area of Science:

• Urology
• Developmental Biology
• Pediatric Surgery

Background:

• Exstrophy-Epispadias Complex (EEC) encompasses rare congenital anomalies affecting urinary, genital, and musculoskeletal systems.
• Understanding the embryological basis of EEC is crucial for managing these complex conditions.

Observation:

• A unique case of EEC presented with a bladder plate, omphalocele, separated pubic bones, and duplicated bladder and urethra.
• This atypical presentation deviates from typical EEC morphology.

Findings:

• Surgical intervention for this variant EEC achieved a favorable outcome.
• The patient demonstrated normal bladder control and voiding post-treatment.

Implications:

• The presented atypical EEC case necessitates a review of existing embryonic theories of exstrophy.
• Further research is needed to refine our understanding of EEC developmental pathways and variations.