Primary Aortic Angiosarcoma: A Review of Two Cases Highlighting Unique Imaging and Clinical Characteristics

Case H Keltner1, Ana Paula Santos Lima1, Malinda West1

  • 1School of Medicine (C.H.K.), Department of Diagnostic Radiology (A.P.S.L., C.F.), Knight Cancer Institute (M.W., L.E.D.), and Department of Orthopaedics & Rehabilitation (K.R.G.), Oregon Health and Science University, 3181 SW Sam Jackson Park Rd, Portland, OR 97239; and Operative Care Division, Portland VA Medical Center, Portland, Ore (K.R.G.).

Summary

Primary angiosarcoma of the aorta, a rare vascular tumor, can present with diffuse arterial tumor emboli causing delayed diagnosis. Careful imaging interpretation is crucial for aortic lesions, especially without atherosclerosis or vasculitis.