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Application of Laparoscopic Partial Splenectomy with Total Blood Flow Occlusion in Benign Splenic Lesions
Published on: December 20, 2024
370
Multiple papillary intralymphatic angioendotheliomas in the spleen
Liping Wang1, Qinglin Yang1, Huihui Zhou2
1Radiology, Yantai Yuhuangding Hospital.
Revista Espanola De Enfermedades Digestivas
|June 15, 2022
Summary
A rare splenic tumor, papillary intralymphatic angioendothelioma (PILA), was identified in an 18-year-old male. Imaging revealed characteristic stellate scars, confirmed by pathology and immunohistochemistry.
Area of Science:
- Vascular oncology
- Spleen pathology
- Diagnostic imaging
Background:
- Papillary intralymphatic angioendothelioma (PILA) is a rare vascular tumor.
- Splenic masses can be asymptomatic and detected incidentally.
Observation:
- An 18-year-old male presented with multiple asymptomatic splenic masses.
- Abdominal MRI showed multiple hypointense lesions with stellate scars on T2WI and contrast-enhanced sequences.
- Lesions exhibited inhomogeneous enhancement and capsular enhancement in the delay phase.
Findings:
- Laparoscopic splenectomy was performed.
- Pathological examination confirmed papillary intralymphatic angioendothelioma (PILA).
- Immunohistochemistry was positive for ERG, CD34, CD31, and D2-40, with a Ki67 index of 3%.
Implications:
- This case highlights the importance of comprehensive imaging and pathological evaluation for diagnosing rare splenic tumors.
- Accurate diagnosis of PILA is crucial for appropriate management and prognosis.
- Further research into PILA's pathogenesis and optimal treatment strategies is warranted.
