Giant aggressive intra-abdominal desmoid-type fibromatosis - case report

Area of Science:

• Oncology
• Surgical Oncology
• Abdominal Surgery

Background:

• Desmoid tumors (DT), also known as aggressive fibromatosis, are rare, locally invasive soft tissue neoplasms.
• They originate from connective tissues and can present as large abdominal masses.
• Symptoms vary based on tumor size and location.

Observation:

• A 68-year-old male presented with a large, asymptomatic 30x40cm intraperitoneal desmoid tumor.
• The tumor encapsulated the medial colic artery, small intestine, and transverse colon.
• Surgical resection involved the tumor, part of the mesentery, 30cm of small intestine, and two-thirds of the transverse colon.

Findings:

• Complete surgical resection of the giant desmoid tumor was achieved.
• The postoperative course was uneventful, with discharge on the 7th day.
• Five-month follow-up showed no signs of tumor recurrence on CT examination.

Implications:

• Aggressive fibromatosis, despite being benign, poses treatment challenges due to its infiltrative nature and high recurrence rate.
• Complete surgical excision is crucial for managing large abdominal desmoid tumors.
• Multidisciplinary approaches may be necessary for optimal patient outcomes.