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[Linear scleroderma in children (apropos of 27 cases)]
Annales De Dermatologie Et De Venereologie
|January 1, 1986
Summary
Linear morphoea is a childhood skin disease predominantly affecting females, often starting abruptly with sclerosis and potential joint or muscle involvement. Early treatment with corticosteroids and physiotherapy shows the best results for this condition.
Area of Science:
- Dermatology
- Rheumatology
- Pediatrics
Context:
- Linear morphoea is a rare childhood connective tissue disease.
- Its etiology remains largely unknown, though trauma and fever are potential triggers.
- The disease presents with characteristic sclerotic skin lesions and can involve deeper tissues.
Purpose:
- To report on 27 cases of linear morphoea and compare them with 218 literature cases.
- To analyze clinical features, laboratory results, and complications of linear morphoea.
- To discuss the potential role of antinuclear antibodies and treatment outcomes.
Summary:
- Linear morphoea primarily affects children, particularly females, with onset around 7-8 years old.
- The condition involves progressive skin sclerosis, often accompanied by musculoskeletal complications like myositis and joint stiffness.
- Antinuclear antibodies are present in some cases, but their significance is unclear; systemic corticosteroids and physiotherapy offer the best treatment results.
Impact:
- This study provides valuable data on the clinical spectrum and progression of linear morphoea.
- It highlights the frequency and impact of musculoskeletal complications, emphasizing the need for integrated management.
- Findings support the classification of linear morphoea within the broader spectrum of scleroderma and inform treatment strategies.