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Remitting Seronegative Symmetrical Synovitis With Pitting Edema in an Adolescent
Joana Baptista de Lima1, Carla Zilhão2, Sérgio Alves2
1Pediatrics, Centro Materno Infantil do Norte Albino Aroso, Centro Hospitalar Universitário do Porto, Porto, PRT.
Remitting seronegative symmetrical synovitis with pitting edema (RS3PE) is a rare condition typically seen in older adults. This report details a unique case of RS3PE diagnosed in a pediatric patient, expanding the known age range for this syndrome.
Area of Science:
- Rheumatology
- Pediatric Rheumatology
- Clinical Case Study
Background:
- Remitting seronegative symmetrical synovitis with pitting edema (RS3PE) is a rare condition typically affecting elderly individuals.
- RS3PE presents with symmetrical tenosynovitis, pitting edema, negative rheumatoid factor, and no erosions.
- The syndrome characteristically responds well to low-dose corticosteroids.
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