Heart Transplantation for Uhl Anomaly in an Adult

Omar Toubat1, Jason J Han1, Jarrod D Predina2

  • 1Division of Cardiovascular Surgery, Department of Surgery, Hospital of the University of Pennsylvania, University of Pennsylvania, Philadelphia, Pennsylvania, USA.

JACC. Case Reports
|April 11, 2024
PubMed
Summary

Uhl anomaly, a rare condition causing right ventricular failure, was successfully treated with heart transplantation in a patient experiencing cardiogenic shock. This case highlights transplantation as a viable option for severe Uhl anomaly.

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