[Fetal intracranial immature teratoma]

Fetal intracranial immature teratomas are extremely rare, rapidly growing and associated with high mortality. We present a case of a large immature intracranial teratoma diagnosed at gestational week 29 with associated macrocephaly and orbital involvement. Due to the tumour size and lethality, cesarean delivery was performed. The neonate died shortly after birth. Postmortem examination and histology confirmed an immature teratoma without somatic-type malignancy. The recurrence risk is considered extremely low.