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Updated: Jan 7, 2026
06:29
Wireless Telemetry Device Implantation in a Fontan Ovine Model for Continuous and Long-Term Hemodynamic Monitoring
Published on: May 2, 2025
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"Failing Fontans:" an emerging challenge in paediatrics.
Tracy Hills1, Erika Mejia2, Rachna May3
1Department of Pediatrics, Vanderbilt University Medical Center, Nashville, TN, USA.
Cardiology in the Young
|December 29, 2025
Summary
As more patients with hypoplastic left heart syndrome survive into adulthood, healthcare providers face challenges managing "failed Fontan" physiology. This case report explores how pediatric palliative care can support these complex adult patients.
Area of Science:
- Pediatric Cardiology
- Palliative Care Medicine
- Congenital Heart Disease Management
Background:
- Staged palliative surgical palliation for hypoplastic left heart syndrome (HLHS) has improved survival rates.
- An increasing number of adults now present with "failed Fontan" physiology, posing unique clinical challenges.
Purpose of the Study:
- To discuss the role and various applications of pediatric palliative care in supporting adult patients with "failed Fontan" physiology.
- To highlight the evolving needs of HLHS survivors into adulthood.
Main Methods:
- This is a brief case report.
- Discussion of clinical management strategies.
- Review of palliative care interventions.
Main Results:
- Providers are increasingly encountering adult patients with "failed Fontan" physiology.
- Pediatric palliative care offers multifaceted support for this population.
- Early integration of palliative care can improve quality of life.
Conclusions:
- The long-term survival of HLHS patients necessitates specialized care models.
- Pediatric palliative care is crucial for managing complex symptoms and improving outcomes in adults with "failed Fontan" physiology.
- Interdisciplinary collaboration is key to addressing the needs of this growing patient group.
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