Pseudomyxoma Peritonei Presenting With Progressive Abdominal Distension and Abdominal Hernia: A Case Report
Menna M Marouf1, Sarah Hady1, Batool Musleh1
1Clinical Sciences, College of Medicine, University of Sharjah, Sharjah, ARE.
Abstract:
Pseudomyxoma peritonei (PMP) is a rare clinical condition characterized by progressive mucinous ascites, most commonly arising from a low-grade appendiceal mucinous neoplasm (LAMN). We report the case of a 53-year-old man with a past medical history of type 2 diabetes mellitus who presented with progressive abdominal distension, constipation, weight loss, and a supraumbilical hernia. Imaging modalities, including ultrasonography, magnetic resonance imaging (MRI), and computed tomography (CT), revealed omental caking, ascites, and hepatic scalloping. Diagnostic laparoscopy revealed mucinous nodules and an abnormal appendiceal tip, and histopathology confirmed LAMN with PMP. The patient had an uneventful recovery following laparoscopic appendectomy and peritoneal biopsies and was referred to a specialized oncology center for consideration of cytoreductive surgery and hyperthermic intraperitoneal chemotherapy (HIPEC). This case highlights the diagnostic challenges of PMP and underscores the importance of early detection and multidisciplinary management to achieve optimal outcomes.
Insights
Pseudomyxoma peritonei (PMP) is a rare condition of mucinous ascites. Early detection and multidisciplinary management, including appendectomy, are crucial for optimal outcomes in patients with low-grade appendiceal mucinous neoplasm (LAMN).
Area of Science:
- Gastroenterology
- Oncology
- Surgical Pathology
Background:
- Pseudomyxoma peritonei (PMP) is a rare condition characterized by mucinous ascites.
- It most commonly originates from a low-grade appendiceal mucinous neoplasm (LAMN).
- PMP presents diagnostic challenges and requires multidisciplinary management.
More Related Videos
20:33A Case Series of Successful Abdominal Closure Utilizing a Novel Technique Combining a Mechanical Closure System with a Biologic Xenograft that Accelerates Wound Healing
Published on: July 4, 2019
10:52Laparoscopic Repair of Para-Esophageal Hernia Using Absorbable Biosynthetic Mesh
Published on: September 11, 2021
Related Concept Videos
Appendicitis-I: Introduction
Etiology: Appendicitis can arise from various causes, primarily rooted in the obstruction of the appendix lumen. Factors contributing to this obstruction include fecal accumulation, lymphoid hyperplasia and, in...
Hiatal Hernia
Intestinal Obstruction I: Introduction
Intestinal Obstruction II: Pathophysiology
Diverticular Disease of the Colon
Appendicitis
