Revisiting RAS family GTPase signaling: effector selectivity and oncogenic bypass

Dhirendra K Simanshu1, Frank McCormick1,2

  • 1NCI RAS Initiative, Cancer Research Technology Program, Frederick National Laboratory for Cancer Research, Frederick, MD, U.S.A.

Insights

RAS GTPases exhibit distinct effector preferences, with canonical RAS binding RAF, RRAS engaging PI3Kα, and RAP activating RalGDS. Oncogenic mutations override these preferences, broadening downstream signaling in cancers.

Area of Science:

  • Molecular Biology
  • Cell Signaling
  • Cancer Biology

Background:

  • Canonical RAS proteins were thought to uniformly bind effectors like RAF, PI3Kα, and RalGDS.
  • Recent findings suggest distinct effector-binding preferences among RAS subfamilies.

Purpose of the Study:

  • To elucidate the specific effector-binding preferences of different RAS GTPase subfamilies.
  • To understand how oncogenic mutations disrupt these preferences and alter downstream signaling.

Main Methods:

  • Quantitative binding assays to measure affinity between RAS proteins and effectors.
  • Structural analysis of effector recognition by RAS GTPases.
  • Analysis of oncogenic RAS mutations and their impact on effector engagement.

Main Results:

  • Canonical RAS (KRAS, HRAS, NRAS) preferentially binds RAF kinases.
  • RRAS subfamily (RRAS2, MRAS) shows high affinity for PI3Kα.
  • RAP subfamily (RAP1A, RAP1B) primarily engages RalGDS.
  • Oncogenic mutations (G12, G13, Q61) disrupt normal hierarchy, enabling canonical RAS to bind PI3Kα and RalGDS.
  • Certain mutations (e.g., KRAS-G12D/V) confer neomorphic PI3Kα binding.

Conclusions:

  • RAS GTPase effector binding is selective, establishing a signaling hierarchy in normal cells.
  • Oncogenic mutations override selectivity, leading to aberrant effector engagement and broadened signaling in cancer.
  • This framework explains RAS-driven cancer signaling by understanding both normal preferences and oncogenic disruptions.

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