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Technique and Patient Selection Criteria of Right Anterior Mini-Thoracotomy for Minimal Access Aortic Valve Replacement
Published on: March 26, 2018
Morquio Syndrome for Aortic Valve Replacement: Anesthesia Concerns - A Case Report.
Jupi Talukdar1, Surekha Vondutla1, Mamatha Munaf1
1Division of Cardiothoracic and Vascular Anaesthesiology, Department of Anesthesiology, Sree Chitra Tirunal Institute for Medical Sciences and Technology, Trivandrum, Kerala, India.
Annals of Cardiac Anaesthesia
|July 13, 2026
Summary
Morquio syndrome, a rare metabolic disorder, presents anesthetic challenges due to airway abnormalities. This case report details a successful anesthetic approach for a patient with Morquio syndrome undergoing aortic valve replacement.
Area of Science:
- Anesthesiology
- Genetics
- Cardiology
Background:
- Morquio syndrome is a lysosomal storage disease.
- Glycosaminoglycan deposition causes skeletal, cardiovascular, and airway issues.
- Airway abnormalities, including thickened mucosa and epiglottis, complicate intubation.
Purpose of the Study:
- To highlight anesthetic challenges in Morquio syndrome.
- To present a different approach to airway management.
- To prepare cardiac anesthesiologists for increased patient numbers.
Main Methods:
- Case report of a patient with Morquio syndrome.
- Severe aortic regurgitation requiring aortic valve replacement.
- Detailed anesthetic management and airway approach.
Main Results:
- Successful anesthetic management was achieved.
- A specific airway management strategy was employed.
- The patient underwent aortic valve replacement.
Conclusions:
- Patients with Morquio syndrome require specialized anesthetic care.
- Airway management strategies must be adapted for these patients.
- Increased survival necessitates preparedness for cardiac surgeries in Morquio syndrome.
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