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Optic atrophy in acute intermittent porphyria.
American Journal of Ophthalmology
|February 1, 1979
Summary
Acute intermittent porphyria can cause blindness due to optic nerve damage. This case highlights potential vision loss and recovery after coma, emphasizing the role of vascular spasm in optic nerve infarction.
Area of Science:
- Neurology
- Ophthalmology
- Genetics
Background:
- Acute intermittent porphyria (AIP) is a rare genetic metabolic disorder.
- AIP attacks can lead to severe neurological complications, including vision loss.