Ectropion of all four eyelids associated with severe ichthyosis congenita: a case report

Ichthyosis congenita associated with severe ectropion of all four eyelids is an extremely uncommon condition and has not previously been reported in a Chinese patient. Our experience of one case shows that a conservative regime of treatment designed to produce a humidified atmosphere combined with the application of local emulsifying agents can help improve the severity of the ectropion. Although these effects tend to be temporary this regime allows surgery to be postponed until the child is older and suitable non-scaly patches of skin can be clearly identified to serve as skin graft donor sites. In this case, full-thickness grafts from each groin were successful. Recurrence of the ectropion required a repetition of the skin grafting 18 months later.