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[Biphasic splenic rupture in a hemophilic child (author's transl)]
Padiatrie Und Padologie
|January 1, 1981
Insights
A delayed splenic rupture occurred in a boy with severe hemophilia B after trauma, despite initial factor IX concentrate treatment. This biphasic rupture highlights the need for careful monitoring in hemophilia patients post-injury.
Area of Science:
- Pediatric Hematology
- Trauma Surgery
- Medical Case Reports
Background:
- Hemophilia B is a rare genetic bleeding disorder.
- Splenic rupture can occur due to trauma.
- Effective management of hemophilia B involves factor replacement therapy.
Observation:
- A 12.5-year-old boy with severe hemophilia B experienced splenic rupture after trauma.
- Initial treatment involved a single dose of factor IX concentrate.
- The patient remained asymptomatic for 9 days post-trauma.
Findings:
- A biphasic splenic rupture was observed, with initial trauma followed by delayed severe abdominal bleeding.
- The single dose of factor IX concentrate may have been insufficient for complete hemostasis.
- This case illustrates a rare complication in hemophilia B management.
Implications:
- Biphasic splenic rupture is a potential delayed complication in hemophilia B patients following trauma.
- Extended monitoring and potentially repeated factor IX concentrate administration may be necessary.
- This case underscores the importance of individualized treatment protocols for trauma in patients with bleeding disorders.
Abstract:
This report describes a biphasic splenic rupture following trauma in a 12 1/2 years old boy with the severe form of hemophilia B. Immediately after the trauma the boy was treated with only one single dose of factor IX concentrate. He stayed free of symptoms for 9 days until finally severe abdominal bleeding occurred.