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Pancreatitis in patients with organic acidemias
S G Kahler1, W G Sherwood, D Woolf
1Department of Pediatrics, Duke University Medical Center, Durham, NC 27710.
The Journal of Pediatrics
|February 1, 1994
Summary
Pancreatitis can be a complication of branched-chain organic acidemias in children. Consider organic acid metabolism disorders in children with unexplained pancreatitis.
Area of Science:
- Biochemistry
- Pediatric Gastroenterology
- Metabolic Disorders
Background:
- Organic acidemias are a group of inherited metabolic disorders.
- Pancreatitis is a known but not widely recognized complication in some organic acidemias.