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[Intranasal encephalocele]
P Clarós1, P Wienberg, A Clarós
1Clínica Clarós, Barcelona (Otorrinolaringología y Cirugía Plástica Facial.
Insights
A rare congenital condition, intranasal encephalocele, presents as a nasal mass with cerebrospinal fluid (CSF) leakage. Surgical treatment via a paralateronasal approach is detailed for this pediatric case.
Area of Science:
- Neurology
- Pediatric Surgery
- Congenital Malformations
Background:
- Intranasal encephaloceles are rare congenital brain herniations through the skull base into the nasal cavity.
- They can present with symptoms like nasal obstruction, CSF rhinorrhea, and recurrent meningitis.
- Early diagnosis and management are crucial to prevent complications.
Abstract:
We present a case of an intranasal encephalocele in a 6-year old girl, that appears as an intranasal mass with CSF rhinorrhea. The surgical treatment is described, specially the extracranial step through a paralateronasal via. The embryogenesis, classification, diagnosis and management of these rare congenital lesions are discussed.