Related Experiment Video
Updated: Jul 30, 2026
09:20
A Mouse Fetal Skin Model of Scarless Wound Repair
Published on: January 16, 2015
Congenital fascial dystrophy: the stiff skin syndrome
Cutis
|October 7, 1997
Abstract:
Congenital fascial dystrophy is an uncommon disorder that may mimic scleroderma. The skin is bound down and feels "wood hard" on palpation of the trunk and extremities. Sclerodactyly, telangiectases, and nail fold changes are not present. Unlike scleroderma, the onset is at birth. Flexion contractures result and other associated abnormalities may include developmental delay and mild hirsutism. We report a typical case to illustrate the clinical and pathologic findings of patients with this disorder.
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