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Cardiac rhabdomyosarcoma: a clinicopathologic and electron microscopy study
A Attanasio1, S Romitelli, A Mauriello
1Dipartimento di Medicina Interna, Università degli Studi Tor Vergata, Roma.
Summary
A rare cardiac rhabdomyosarcoma caused a stroke in a 66-year-old woman. This tumor led to neurological symptoms, including ataxia and diplopia, ultimately resulting in a fatal stroke.
Area of Science:
- Cardiology
- Neurology
- Oncology
Background:
- A 66-year-old woman presented with neurological deficits including ataxia and diplopia.
- Brain MRI revealed an ischemic medullary lesion, suggesting a cerebrovascular event.
Observation:
- Cardiac examination noted a systolic murmur and echocardiography showed mild mitral regurgitation with an enlarged posterior papillary muscle.
- The patient experienced a sudden fatal stroke two weeks after admission.
Findings:
- Autopsy confirmed a recent cerebral infarction and old splenic infarcts.
- A cardiac examination revealed a left ventricular mass, histologically identified as rhabdomyosarcoma.
Implications:
- This case highlights the potential for cardiac rhabdomyosarcoma to cause embolic stroke.
- Early detection and understanding of rare cardiac tumors are crucial for managing neurological complications.