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Intestinal leiomyosarcoma and gastroparesis associated with von Recklinghausen's disease
V Bernardis1, D Sorrentino, D Snidero
1Gastrointestinal Unit, Department of Clinical and Experimental Pathology, University of Udine Medical School, Udine, Italy.
Digestion
|January 20, 1999
Abstract:
The rare association between intestinal leiomyosarcoma, von Recklinghausen's disease (type-1 neurofibromatosis) and gastroparesis is described. A 20-year-old male, diagnosed 12 years earlier as having pelvic von Recklinghausen's disease, presented with nausea and vomiting. A gastric scintigraphy demonstrated an extremely slow gastric emptying time in the absence of obvious causes for gastroparesis. A small ileal leiomyosarcoma was later found and removed by surgery. The latter was followed by a marked improvement in the clinical condition of the patient.