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Foix-Chavany-Marie syndrome.
1Department of Neurology, Taipei Municipal Chung-Hsin Hospital, ROC. annmy@gcn.net.tw
Zhonghua Yi Xue Za Zhi = Chinese Medical Journal; Free China Ed
|January 5, 2002
Summary
Foix-Chavany-Marie syndrome (FCMS) involves facial and swallowing paralysis. This case highlights FCMS resulting from multiple strokes affecting brain regions controlling speech and movement.
Area of Science:
- Neurology
- Neuroimaging
- Cerebrovascular Disease
Background:
- Foix-Chavany-Marie syndrome (FCMS) is a rare neurological disorder characterized by suprabulbar palsy.
- It presents with anarthria and paralysis of facial, lingual, pharyngeal, and masticatory muscles, with a dissociation between automatic and voluntary movements.
- The cortico-subcortial type of suprabulbar palsy, FCMS, is often linked to lesions in the opercular regions.
Observation:
- A 64-year-old male presented with acute speechlessness.
- Clinical examination revealed classic signs of FCMS.
- Cranial MRI identified a right opercular lesion and multiple bilateral lacunar infarcts.
Findings:
- Hexamethylen-propylene amine oxime (HMPAO) brain SPECT demonstrated hypoperfusion in bilateral opercular areas, more pronounced on the right.
- The findings suggest FCMS in this patient resulted from multiple cerebrovascular insults affecting bilateral cortico-subcortial opercular regions.
- Stroke in the opercular region is the most common etiology for FCMS.
Implications:
- This case underscores the role of multiple cerebrovascular events in the pathogenesis of FCMS.
- Neuroimaging techniques like MRI and SPECT are crucial for diagnosing FCMS and identifying underlying vascular causes.
- Understanding the specific vascular territories affected can aid in predicting prognosis and management strategies for FCMS.