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Hemimacroglossia caused by isolated plexiform neurofibroma: a case report.
Ender Guclu1, Abdurrahman Tokmak, Fatih Oghan
1Department of Otorhinolaryngology and Head and Neck Surgery, Duzce Faculty of Medicine, University of Abant Izzet Baysal, Duzce, Turkey.
The Laryngoscope
|February 17, 2006
Summary
This case report details a rare isolated plexiform neurofibroma of the tongue in a child, successfully treated with intraoral surgery. The intraoral approach offers good exposure for complete tumor removal with minimal complications.
Area of Science:
- Oncology
- Surgical Pathology
- Pediatric Surgery
Background:
- Plexiform neurofibromas are rare benign tumors.
- Isolated tongue neurofibromas, not associated with neurofibromatosis, are exceptionally rare.
- These tumors can cause significant macroglossia and functional impairment.
Observation:
- A case of a 5-year-old girl with a diffuse, isolated plexiform neurofibroma of the tongue is presented.
- The tumor infiltrated the tongue base, leading to macroglossia.
- No association with neurofibromatosis was identified.
Findings:
- Intraoral surgery provided adequate exposure for complete tumor excision.
- The surgical approach resulted in limited postoperative sequelae.
- This method is a viable alternative for treating isolated tongue plexiform neurofibromas.
Implications:
- Intraoral surgery is a feasible and effective treatment for isolated plexiform neurofibroma of the tongue.
- Early diagnosis and surgical intervention are crucial to prevent progressive functional deficits.
- This case highlights the importance of considering rare diagnoses in pediatric head and neck masses.