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Updated: Jul 18, 2026
13:26
Measuring Connectivity in the Primary Visual Pathway in Human Albinism Using Diffusion Tensor Imaging and Tractography
Published on: August 11, 2016
Woakes' syndrome and albinism
Marco Caversaccio1, Ariane Baumann, Arthur Helbling
1Department of ENT, Head and Neck Surgery, University Hospital, Inselspital, 3010 Bern, Switzerland. marco.caversaccio@insel.ch
Auris, Nasus, Larynx
|December 22, 2006
Summary
Nasal polyposis without eosinophils, a form of Woakes' syndrome, presents treatment challenges. Radiotherapy was effective for a severe case resistant to conventional therapies.
Area of Science:
- Otolaryngology
- Dermatology
- Oncology
Background:
- Nasal polyposis is a common, multifactorial condition.
- Eosinophil-rich polyps respond well to corticosteroids.
- Polyps lacking eosinophils present significant therapeutic difficulties.
Observation:
- A case of extreme Woakes' syndrome in a 29-year-old albino patient is presented.
- This syndrome involves severe, recurrent nasal polyps, often histologically lacking eosinophils, and nasal broadening.
- The patient's fibrotic polyps were resistant to medical and surgical interventions.
Findings:
- Radiotherapy was employed as a subsequent treatment modality.
- The case highlights the challenges in managing non-eosinophilic nasal polyps.
- The interplay between Woakes' syndrome and albinism was considered.
Implications:
- This case underscores the need for alternative treatment strategies for refractory nasal polyps.
- Radiotherapy may be a viable option for severe, treatment-resistant cases.
- Further research into the pathoetiology of non-eosinophilic polyps and associated conditions is warranted.
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