[Wolfram syndrome: four case reports]
H Skiker1, N Boutimzine, B Ouazani
1Service d'Ophtalmologie A- Hôpital des Spécialités Rabat, Maroc. h.skiker@yahoo.fr
Bulletin De La Societe Belge D'Ophtalmologie
|February 7, 2008
Abstract:
Wolfram syndrome, also known as DIDMOAD syndrome, is a rare disease characterized by the association of diabetes mellitus, diabetes insipidus, optic atrophy and deafness. The ophthalmologic findings are largely dominated by optic atrophy. Through four cases and a literature review, the authors describe the ophthalmologic findings in this disease and its clinical and genetic aspects.
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