Isolated left ventricular noncompaction causing stroke in a 30-year-old woman: case report and literature review

Giselle A Baquero1, Dustin J Colegrove, Javier E Banchs

  • 1Penn State Hershey Heart and Vascular Institute, Hershey, Pennsylvania 17033-0850, USA. gbaquero@hmc.psu.edu

Insights

Isolated left ventricular noncompaction, a rare heart condition, can lead to stroke. This case highlights the need for better prevention strategies for thromboembolic events in affected patients.

Area of Science:

  • Cardiology
  • Neurology

Background:

  • Isolated left ventricular noncompaction (ILVNC) is a rare cardiomyopathy.
  • It presents with prominent ventricular trabeculations and intertrabecular recesses.
  • Clinical issues include heart dysfunction, conduction problems, and embolic events.

Observation:

  • A 30-year-old woman with a history of hypertrophic cardiomyopathy experienced an ischemic stroke.
  • She was diagnosed with isolated left ventricular noncompaction.
  • Thrombus formation in recesses is the suspected cause of embolic events.

Findings:

  • Evidence-based guidelines for preventing thromboembolic events in ILVNC are lacking.
  • This case underscores the potential link between ILVNC and cerebrovascular events.
  • Literature review on ILVNC and associated embolic phenomena.

Implications:

  • Further research is needed to establish preventative measures for thromboembolic events in ILVNC.
  • Early diagnosis and management of ILVNC may reduce stroke risk.
  • This case highlights the importance of considering ILVNC in young stroke patients.

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