Pilomatrixoma: A Rare Cause of Midline Neck Swelling

Pilomatrixoma is a uncommon benign neoplasm of hair matrix origin, with usual occurrence in the head and neck region. It has bimodal age of occurrence, first peek is seen in children and the second in elderly in sixth decade. In this case, we report a case of a young boy presenting with midline neck swelling with differential diagnosis of sebaceous cyst, thyroglossal cyst or dermoid cyst. Definitive diagnosis was not made until the final histopathology report was available after complete excision. Accurate diagnosis and appropriate treatment is essential to obviate the minimal risk of recurrence or very rare malignant transformation. A high index of suspicion is required to diagnose this tumor, especially in unusual locations as in this case.