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[Linear scleroderma "en coup de sabre" causing severe neurological and ocular symptoms]
Hannah Stroh1, Christoph Jaschinski2, Alexander Enk3
1Haut- und Laserzentrum Heidelberg, Bergheimer Str. 56a, 69115, Heidelberg, Deutschland. hannah_stroh@yahoo.com.
Summary
This rare case study details the successful treatment of a 4-year-old girl with linear scleroderma "en coup de sabre" (LSECDS) involving forehead lesions, uveitis, and seizures.
Area of Science:
- Pediatric Rheumatology
- Dermatology
- Neurology
Background:
- Linear scleroderma "en coup de sabre" (LSECDS) is a rare autoimmune condition.
- Severe extracutaneous manifestations, including ocular and neurological involvement, pose significant treatment challenges.
- A 4-year-old girl presented with characteristic forehead sclerotic lesions, uveitis, and epileptic seizures.
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