A rare case of retroperitoneal primitive neuroectodermal tumor (PNET)

Retroperitoneal primitive neuroectodermal tumors (PNET) is a rare neoplastic disease of high malignancy with a tendency towards early metastasis, affect young adults irrespective of the gender. We present 81 year old woman, who was admitted in the Urology Department with symptoms of right flank pain and hematuria. Contrast-enhanced computerized tomography scan (CT-scan) showed a large heterogeneous right kidney mass around 12 cm in diameter. The final diagnosis of primitive neuroectodermal tumor (PNET) was established based on clinical, pathological, and molecular results.