[Orbital melanotic neuroectodermal tumor in an infant].

Area of Science:

• Ophthalmology
• Pediatric Oncology
• Pathology

Background:

• Orbital tumors are rare in infants.
• Melanotic neuroectodermal tumors (MNTs) are uncommon neoplasms of neural crest origin.

Purpose of the Study:

• To report a case of a rapidly progressive orbital mass in an infant.
• To describe the diagnostic and histopathological findings of a melanotic neuroectodermal tumor in a pediatric patient.

Main Methods:

• Clinical presentation and imaging (B-scan, orbital CT) were analyzed.
• Surgical excision of the orbital mass was performed.
• Histopathological and immunohistochemical examinations confirmed the diagnosis.

Main Results:

• A rapidly growing, hard, irregular superolateral orbital mass was identified.
• Imaging revealed a soft tissue mass involving bone and the lacrimal gland.
• Histology confirmed a melanotic neuroectodermal tumor.

Conclusions:

• Melanotic neuroectodermal tumor is a rare but treatable cause of pediatric orbital masses.
• Early diagnosis and surgical management are crucial for favorable outcomes.
• Complete surgical excision resulted in no recurrence in this case.