[Sarcoma with intracranial component misdiagnosed as subcutaneous lipoma]

We present a case story of a sarcoma, misdiagnosed as a subcutaneous lipoma, with an intracranial component. The patient developed a painless tumour less than 5 cm in diameter within a few months. An attempt of removing the tumour in local anaesthetic was stopped during the procedure as the intracranial component became evident. At a later stage, the sarcoma was removed surgically with wide local excision, local flap reconstruction and postoperative proton therapy. Six months later, the patient was well, with no clinical signs or evidence on imaging of recurrence of the sarcoma.