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A Novel Approach for the Administration of Medications and Fluids in Emergency Scenarios and Settings
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[Enzymotherapy infusion in home hospital care]

Loïse Padioleau1

  • 1Hospitalisation à domicile, Unité de soins pédiatrique, AP-HP, 14 rue Vesale, 75005 Paris, France.

Soins. Pediatrie, Puericulture
|October 9, 2023
PubMed

Insights

Home hospitalization services empower families to administer enzyme replacement therapy for pediatric enzyme-deficiency diseases, reducing nurse time while ensuring safe, quality care.

Area of Science:

  • Pediatric Hematology/Oncology
  • Pharmacology
  • Nursing Practice

Context:

  • The Assistance publique - Hôpitaux de Paris home hospitalization service cares for 150 children daily across six units.
  • A subset of these children receive enzyme replacement therapy for rare enzyme-deficiency diseases.
  • Treatment involves lengthy weekly intravenous infusions requiring significant nursing resources.

Purpose:

  • To develop a standardized procedure for enzyme replacement therapy administration.
  • To reduce the time burden on nursery nurses.
  • To enhance patient and family involvement in treatment delivery.

Summary:

  • A multidisciplinary team developed a protocol to harmonize enzyme replacement therapy practices.
  • This initiative aims to empower families to administer injections, optimizing care delivery.
  • The procedure focuses on maintaining high standards of care quality and patient safety.

Impact:

  • Potential reduction in healthcare resource utilization.
  • Improved patient quality of life through home-based treatment.
  • Enhanced capacity for managing pediatric enzyme-deficiency diseases within home care settings.

Keywords:
autonomisationempowermentenzyme infusionhospitalisation à domicilehospitalization at homeparentperfusion d’enzymothérapieprocedureprocédure

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