Rare association between giant-cell aortitis and giant-cell aortic valvulitis
Georgina Del Cisne Jadán Luzuriaga1, Ricardo Ribeiro Dias2, José Augusto Duncan Santiago2
1Universidade de São Paulo, Faculdade de Medicina, Instituto do Coração, Departamento de Miocardiopatias e Doenças da Aorta, São Paulo, SP, Brasil.
Giant cell arteritis (GCA) can involve the aorta, but giant cell aortic valvulitis is rare. This case highlights a patient with aortic aneurysm and valvular insufficiency due to associated giant cell aortitis and valvulitis.
Area of Science:
- Cardiovascular Pathology
- Rheumatology
- Vascular Inflammation
Background:
- Giant cell arteritis (GCA) is a systemic vasculitis affecting medium and large arteries.
- Aortic involvement and aneurysm formation are known complications of GCA.
- Giant cell involvement of the aortic valve is an infrequent finding.
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